Familial porokeratosis of Mibelli: A peerless entity

Authors

  • Yugandar Inakanti

DOI:

https://doi.org/10.66344/jpad.25.2.2015.98

Keywords:

Ala nasi, cornoid lamella, finger, parakeratosis, porokeratosis

Abstract

Porokeratosis are a group of hereditary or acquired disorders characterized by annular plaques with an atrophic centre and a hyperkeratotic peripheral ridge. Pathologically, porokeratosis is characterized by a column of parakeratotic cells, called the cornoid lamella. This report describes a 55-year-old male with his two sons affected by porokeratosis of Mibelli and it was confirmed histopathologically. The rarity of this disorder in family, its clinical exuberance and the destructive character of the lesions, as well as, nasal, finger and abdomen involvement were unusual in case of porokeratosis.

References

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Published

2016-11-19

How to Cite

1.
Inakanti Y. Familial porokeratosis of Mibelli: A peerless entity. J Pak Assoc Dermatol [Internet]. 2016Nov.19 [cited 2026Apr.30];25(2):144-7. Available from: https://www.jpad.com.pk/index.php/jpad/article/view/98

Issue

Vol. 25 No. 2 (2015): April - June

Section

Case Reports

License

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Authors retain the copyright to their work and grant the 'Journal of Pakistan Association of Dermatologists (JPAD)' the right of first publication under a Creative Commons Attribution 4.0 International (CC BY 4.0) license. This license allows others to share, adapt, and reuse the work for any purpose, including commercial use, as long as appropriate credit is given to the original authors and the journal.

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