Segmental neurofibromatosis (a rare variant of a common genodermatosis): report of two cases

Authors

  • Arfan ul Bari Dermatology Department, Combined Military Hospital, Muzaffarabad, Azad Jammun Kashmir
  • Simeen Ber Rahman Dermatology Department, Military Hospital, Rawalpindi

DOI:

https://doi.org/10.66344/jpad.v16i2.858

Keywords:

Neurofibromatosis, segmental neurofibromatosis, neurofibroma

Abstract

Segmental neurofibromatosis is a rare variant of neurofibromatosis in which the lesions are confined to one segment or dermatome of the body. They resemble classical neurofibromas in their morphology, histopathology. However, systemic associations are usually absent. We report two cases representing with segmental distribution of neurofibromas on localized areas of the skin over back and chin respectively. They had negative family history and were lacking any systemic involvement.

References

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Published

03.01.2017

Issue

Vol. 16 No. 2 (2006): April - June

Section

Case Reports

License

Copyright (c) 2017 Arfan ul Bari, Simeen Ber Rahman

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This work is licensed under a Creative Commons Attribution 4.0 International License.

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Authors retain the copyright to their work and grant the 'Journal of Pakistan Association of Dermatologists (JPAD)' the right of first publication under a Creative Commons Attribution 4.0 International (CC BY 4.0) license. This license allows others to share, adapt, and reuse the work for any purpose, including commercial use, as long as appropriate credit is given to the original authors and the journal.

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How to Cite

1.
Segmental neurofibromatosis (a rare variant of a common genodermatosis): report of two cases. J Pak Assoc Dermatol [Internet]. 2017 Jan. 3 [cited 2026 Aug. 2];16(2):108-11. Available from: https://www.jpad.com.pk/index.php/jpad/article/view/858