Multiple familial trichoepitheliomas
DOI:
https://doi.org/10.66344/jpad.15.2.2005.642Keywords:
Trichoepithelioma, familial.Abstract
Trichoepithelioma (TE) is a benign cutaneous tumor that originates from hair follicles and
occurs either in multiple or solitary forms. Multiple familial trichoepitheliomas (MFT) is
transmitted as an autosomal dominant trait, and a region at 9p21 is thought to be involved in
the tumorigenesis. Solitary TE occurs more commonly than multiple TE, is not inherited and
rarely seen in perianal region. We present a family with MFT, of which several members;
both male and female were affected. The tumor is benign but is important to recognize
because of histopathological significance.
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