Multiple familial trichoepitheliomas
Keywords:
Trichoepithelioma, familial.Abstract
Trichoepithelioma (TE) is a benign cutaneous tumor that originates from hair follicles andoccurs either in multiple or solitary forms. Multiple familial trichoepitheliomas (MFT) istransmitted as an autosomal dominant trait, and a region at 9p21 is thought to be involved inthe tumorigenesis. Solitary TE occurs more commonly than multiple TE, is not inherited andrarely seen in perianal region. We present a family with MFT, of which several members;both male and female were affected. The tumor is benign but is important to recognizebecause of histopathological significance.References
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