Acute febrile neutrophilic dermatosis (Sweet syndrome) in childhood: two case report and review

Authors

  • Mohammad Taghi Noorbala
  • Ali Fatahi Bafghi

Keywords:

Sweet syndrome, septicemia, children, corticosteroid

Abstract

Sweet syndrome is rare in children. Usually, heralded by tender polymorphous skin lesions, typically accompanied by fever and peripheral neutrophilia, can easily be mistaken for infection and lead to many antibiotic administration. Such therapy does not improve disease, which is thought to represent an immunologic reaction to agents as diverse as infection, neoplasia, or drugs.We report two boys, six and nine-year-old who suffered from acute febrile neutrophilic dermatosis. Both were febrile, had leukocytosis, and exhibited characteristic clinical and histopathologic lesions. They had an antecedent trauma, and responded to systemic corticosteroids. Our evaluation and long term follow-up of these children failed to reveal evidence of underlying malignancy or a chronic systemic illness typically encountered in Sweet syndrome. 

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Published

2016-12-21

How to Cite

1.
Noorbala MT, Bafghi AF. Acute febrile neutrophilic dermatosis (Sweet syndrome) in childhood: two case report and review. J Pak Assoc Dermatol [Internet]. 2016Dec.21 [cited 2024Nov.8];20(2):106-11. Available from: https://www.jpad.com.pk/index.php/jpad/article/view/401

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Case Reports