Circumscribed juvenile type pityriasis rubra pilaris (type 4): are we missing them?

Authors

  • Sankha Koley
  • Sanjiv Choudhary
  • Atul Salodkar
  • Jyotyrindranath Sarkar
  • Manoj Choudhary

Keywords:

Pityriasis rubra pilaris, circumscribed juvenile type, palmoplantar keratoderma

Abstract

Pityriasis rubra pilaris (PRP) is a rare disease. The lack of pathognomonic features and specific clinical or diagnostic features often make identification of PRP very difficult. PRP type 4 (circumscribed juvenile type) is characterized by scaly plaques on elbows, knees and palmoplantar keratoderma. Sometimes these lesions may become extremely difficult to differentiate from those of psoriasis. We report 3 cases of PRP type 4, noted in just 5 months. We feel PRP, specially the type 4, is not so rare in Indian subcontinent. A good clinical knowledge and high index of suspicion may help to identify more cases. 

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Published

2016-12-21

How to Cite

1.
Koley S, Choudhary S, Salodkar A, Sarkar J, Choudhary M. Circumscribed juvenile type pityriasis rubra pilaris (type 4): are we missing them?. J Pak Assoc Dermatol [Internet]. 2016Dec.21 [cited 2024Nov.8];20(2):98-102. Available from: https://www.jpad.com.pk/index.php/jpad/article/view/399

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Case Reports

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