Inflammatory linear verrucous epidermal nevus: a rare experience

Authors

  • Haresh Kumar Department of Dermatology Shaheed Mohatarma Benazir Bhutto Medical University Larkana, Sindh.
  • Irfan Ahmed Shaikh Department of Dermatology Shaheed Mohatarma Benazir Bhutto Medical University Larkana, Sindh
  • Naeem Soomro Department of Dermatology Shaheed Mohatarma Benazir Bhutto Medical University Larkana, Sindh
  • Mehran Bukhari Department of Dermatology Shaheed Mohatarma Benazir Bhutto Medical University Larkana, Sindh
  • Akhter Bhutto Department of Dermatology Shaheed Mohatarma Benazir Bhutto Medical University Larkana, Sindh

DOI:

https://doi.org/10.66344/jpad.v32i1.1801

Abstract

Inflammatory linear verrucous epidermal nevus ( ILVEN ) is caused by unknown postzygotic mutation rescued by genetic mosaicism. It presents as intensely pruritic, erythematous, psoriasiform and verrucous, papules which coalesce to form plaques along the lines of Blaschko, mostly involving a single leg. It has usually early life onset. However, since its first description, very few cases have been reported which were of adult onset. Herein, we present a case of ILVEN in a 22 year old male patient.

Author Biography

  • Haresh Kumar, Department of Dermatology Shaheed Mohatarma Benazir Bhutto Medical University Larkana, Sindh.

    Abstract

    Inflammatory linear verrucous epidermal nevus is an uncommon variant of epidermal nevus, caused by unknown postzygotic mutation rescued by genetic mosaicism. Clinically, it presents as intensely pruritic, erythematous, psoriasiform and verrucous, papules and plaques following the lines of Blaschko, mostly involving the single leg. It has usually early life onset. However, since its first description, very few cases have been reported which were of adult onset. Herein, we report a case of ILVEN in a 22 year old male.

References

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Published

29.03.2022

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Section

Case Reports

How to Cite

1.
Inflammatory linear verrucous epidermal nevus: a rare experience. J Pak Assoc Dermatol [Internet]. 2022 Mar. 29 [cited 2026 Oct. 19];32(1):191-4. Available from: https://www.jpad.com.pk/index.php/jpad/article/view/1801