Successful treatment of Epidermolysis Bullosa Pruriginosa with Cyclosporine
DOI:
https://doi.org/10.66344/jpad.v32i1.1786Abstract
Epidermolysis bullosa (EB) pruriginosa is a rare clinical subtype of dystrophic epidermolysis bullosa (DEB) that is characterized by intense pruritus resulting in hypertrophic, lichenified, prurigo-like plaques and nodules secondary to scratching. The variability in the age of onset, rarity of intact bullae, histologic ambiguities and close resemblance to other conditions such as acquired inflammatory dermatoses may make diagnosis difficult for this unusual condition. In this report, we describe a case of 23 years old male who presented with blistering and pruritus with no family history of the disease. He had taken multiple medications without much relief so we gave him Cyclosporine which proved to be effective in relieving his symptoms and blistering.
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