Neurological Manifestations of progressive hemifacial atrophy-case report

Abstract

Progressive hemifacial atrophy is a rare, unilateral, atrophic craniofacial form of morphea involving the dermis, subcutaneous tissue, fat, muscle, and even bone. We report a case of a child having progressive hemifacial atrophy, presented with rapidly progressive neurological symptoms and associated radiological manifestations. In this case of hemifacial atrophy, the sensitivity of MRI in detecting intracranial lesions is demonstrated. Recommendations for imaging these patients are proposed.