Multiple familial trichoepitheliomas: A rare autosomal dominant skin tumor

Authors

  • Saba Latif PNS Shifa Hopital,Karachi

DOI:

https://doi.org/10.66344/jpad.31.3.2021.1646

Keywords:

Familial, Trichoepithelioma, Basal cell carcinoma, Benign facial tumors, Appendageal tumors, Autosomal Dominant

Abstract

Multiple familial trichoepithelioma (MFT) is a rare autosomal dominant skin disease that presents as multiple small tumors, predominantly on face. The lesions resemble other types of skin diseases that present with papules and nodules. We present a patient with persistent eruptions of asymptomatic but cosmetically disfiguring papulonodular lesions on her face which histologically proved as lesions of trichoepitheioma. There was history of similar lesions in other family members too. She was managed with serial electrocautery, chemical cautery and medium depth chemical peel sessions.

References

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Published

2022-04-10

How to Cite

1.
Latif S. Multiple familial trichoepitheliomas: A rare autosomal dominant skin tumor. J Pak Assoc Dermatol [Internet]. 2022Apr.10 [cited 2026Apr.22];31(3):546-9. Available from: https://www.jpad.com.pk/index.php/jpad/article/view/1646

Issue

Vol. 31 No. 3 (2021): July - September

Section

Case Reports

License

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Authors retain the copyright to their work and grant the 'Journal of Pakistan Association of Dermatologists (JPAD)' the right of first publication under a Creative Commons Attribution 4.0 International (CC BY 4.0) license. This license allows others to share, adapt, and reuse the work for any purpose, including commercial use, as long as appropriate credit is given to the original authors and the journal.

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