Congenital adrenal hyperplasia with polycystic ovarian disease: A rare cause of hirsutism

Authors

  • Shazia Rasul Department of Obstetrics & Gynecology, Shalamar Hospital, Lahore
  • Lubna Riaz Dar Department of Obstetrics & Gynecology, Shalamar Hospital, Lahore
  • Abdul Hameed Department of Dermatology, Naseer Hospital, New Garden Town, Lahore

DOI:

https://doi.org/10.66344/jpad.v20i3.414

Keywords:

Hirsutism, non-classical congenital adrenal hyperplasia, polycystic ovarian disease

Abstract

Hirsutism may be defined as presence of terminal hairs in women with a male-like pattern of distribution. Hirsutism is related to serum androgen and cutaneous sensitivity to other hormones. The most prevalent causes of hirsutism are polycystic ovary syndrome and isolated hirsutism. Non-classical congenital adrenal hyperplasia (21-hydroxylase deficiency) and drug induced type are less frequent rather rare causes. Diagnostic evaluations should address identifying etiology and its associated co-morbidities to properly manage the patients. We present a case of 22-year-old unmarried female who presented with hirsutism and on detailed evaluation she was diagnosed as a case of nonclassical adrenal hyperplasia and polycystic ovaries. Along with laser hair removal, proper treatment of underlying etiology led to reversal of her symptoms.

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Published

21.12.2016

Issue

Section

Case Reports

How to Cite

1.
Congenital adrenal hyperplasia with polycystic ovarian disease: A rare cause of hirsutism. J Pak Assoc Dermatol [Internet]. 2016 Dec. 21 [cited 2026 Jul. 27];20(3):176-9. Available from: https://www.jpad.com.pk/index.php/jpad/article/view/414