Papillon-Lefevre syndrome: case report

Authors

  • Ghasem Rahmatpour Rokni
  • Tahereh Karimi
  • Mahnaz Sharifian

DOI:

https://doi.org/10.66344/jpad.27.2.2017.1091

Keywords:

Papillon–Lefevre syndrome

Abstract

Papillon-Lefevre syndrome (PLS) is a rare genodermatosis of autosomal recessive inheritance manifesting as palmoplantar hyperkeratosis with periodontitis. A 4-year old Iranian girl was referred to the Mazandaran University Hospital, Sari complaining of well-demarcated, psoriasiform, yellowish, keratotic plaques over the skin of her palms and soles with transgrediens. For cutaneous lesions, she was treated with oral acitretin 0.5 mgâ„kgâ„day and topical keratolytic 5% salicylic acid in combination with 10% urea. 

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Published

2018-07-11

How to Cite

1.
Rokni GR, Karimi T, Sharifian M. Papillon-Lefevre syndrome: case report. J Pak Assoc Dermatol [Internet]. 2018Jul.11 [cited 2026Apr.30];27(2):187-91. Available from: https://www.jpad.com.pk/index.php/jpad/article/view/1091

Issue

Vol. 27 No. 2 (2017): April - June

Section

Case Reports

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