Epidermodysplasia verruciformis: a rare genodermatosis with risk of malignant transformation

Authors

  • Arfan ul Bari
  • Rifat Yasmin
  • Afaq Ahmed

Keywords:

Epidermodysplasia verruciformis, human papillomavirus, verruca plana

Abstract

Epidermodysplasia verruciformis is a rare, lifelong, autosomal recessive hereditary disorder affecting the skin and is characterized by chronic infection with human papillomavirus. We report a case of young boy who presented with widespread pityriasis versicolor-like lesions and was mistreated as fungal infection for some time. A brief review of the condition is also given below.  

References

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Oliveira WRP, Carrasco S, Festa C et al. Nonspecific cell-mediated immunity in patients with epidermodysplasia verruciformis. J Dermatol 2003; 30: 203-9.

Purdie KJ, Surentheran T, Sterling JC et al. Human papillomavirus gene expression in cutaneous squamous cell carcinomas from immunosuppressed and immunocompetent individuals. J Invest Dermatol. 2005; 125: 98-107.

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Micali G, Nasca MR, Dall'Oglio F, Musumeci ML. Cimetidine therapy for epidermodisplasia verruciformis. J Am Acad Dematol 2003; 48: S9-S10.

Anadolu R, Oskay T, Erdem C, Boyvat A et al. Treatment of epidermodysplasia verruciformis with a combination of acitretin and interferon alfa-2a. J Am Acad Dermatol 2001; 45: 296-9.

Oliveira WR, Festa C, Rady P, Tyring SK. Seborrheic keratosis-like lesions in patients with epidermodysplasia verruciformis. J Dermatol 2003; 30: 48-53.

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Published

2017-01-03

How to Cite

1.
Bari A ul, Yasmin R, Ahmed A. Epidermodysplasia verruciformis: a rare genodermatosis with risk of malignant transformation. J Pak Assoc Dermatol [Internet]. 2017Jan.3 [cited 2024May19];16(4):242-5. Available from: http://www.jpad.com.pk/index.php/jpad/article/view/891

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