Epidermodysplasia verruciformis: a rare genodermatosis with risk of malignant transformation
Keywords:
Epidermodysplasia verruciformis, human papillomavirus, verruca planaAbstract
Epidermodysplasia verruciformis is a rare, lifelong, autosomal recessive hereditary disorder affecting the skin and is characterized by chronic infection with human papillomavirus. We report a case of young boy who presented with widespread pityriasis versicolor-like lesions and was mistreated as fungal infection for some time. A brief review of the condition is also given below. ÂReferences
Joblonska S. Epidermodysplasia verruciformis. In: Friedman RJ, ed. Skin Cancers. Philadelphia: WB Saunders; 1991. p. 101-13.
Lutzner MA, Blanchet-Bardon C, Orth G. Clinical observations, virologic studies, and treatment trials in patients with epidermodysplasia verruciformis, a disease induced by specific human papillomaviruses. J Invest Dermatol 1984; 83: 18s-25s.
Oliveira WRP, Carrasco S, Festa C et al. Nonspecific cell-mediated immunity in patients with epidermodysplasia verruciformis. J Dermatol 2003; 30: 203-9.
Purdie KJ, Surentheran T, Sterling JC et al. Human papillomavirus gene expression in cutaneous squamous cell carcinomas from immunosuppressed and immunocompetent individuals. J Invest Dermatol. 2005; 125: 98-107.
Majewski S, Jablonska S. Epidermodysplasia verruciformis as a model of human papillomavirus-induced genetic cancer of the skin. Arch Dermatol 1995; 131: 1312-8
Micali G, Nasca MR, Dall'Oglio F, Musumeci ML. Cimetidine therapy for epidermodisplasia verruciformis. J Am Acad Dematol 2003; 48: S9-S10.
Anadolu R, Oskay T, Erdem C, Boyvat A et al. Treatment of epidermodysplasia verruciformis with a combination of acitretin and interferon alfa-2a. J Am Acad Dermatol 2001; 45: 296-9.
Oliveira WR, Festa C, Rady P, Tyring SK. Seborrheic keratosis-like lesions in patients with epidermodysplasia verruciformis. J Dermatol 2003; 30: 48-53.