Porokeratosis of Mibelli: an uncommon genodermatosis
Keywords:
Porokeratosis, porokeratosis of MibelliAbstract
Porokeratosis of Mibelli is an uncommon, inherited, autosomal dominant disorder characterized by disordered epidermal keratinization and by a predisposition to develop malignant transformation. A case of this rare disorder with classical presentation in a teen aged boy is reported here, which was managed with topical retinoid, superficial chemical peeling and sunscreen lotion.ÂReferences
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