Keratosis lichenoides chronica: case report

Authors

  • Sunil Kumar Gupta
  • Dr. Monika
  • Dr. Deepika

Keywords:

Keratosis lichenoides chronica

Abstract

Keratosis lichenoides chronica (KLC) or Nekam’s disease is a controversial rare dermatosis of  unknown etiology. It is characterized by symmetrically arranged lichenoid linear and reticulate  scaly plaques and hyperkeratotic papules most marked on extremities and buttocks and  accompanied by facial lesions resembling seborrheic dermatitis.It usually affects adults between 20  to 40 years but children are affected occasionally. We report a case of middle-aged female showing  chronic lichenoid plaques in a characteristic linear and reticulate fashion over buttocks and thighs  with minimal pruritus, resistant to conventional treatment, and associated seborrheic dermatitis like  eruption on face. KLC is a chronic and progressive disorder extending over many years and is very  resistant to therapeutic approaches. Despite being a rare disorder, it is important to be familiar with  KLC, which can be easily confused with koebner’s phenomena of lichen planus.

References

Ghislain PD, De Bier A, Creusy C, Modiano P. Keratosis lichenoides chronica: report of a new case, with success of PUVA therapy. Dermatol Online J. 2001;7:4-8.

Breathnach SM.Lichen planus and lichenoid disorders. In: Burns T, Breathnach S, Cox N, Griffiths C, editors. Rook’s Textbook of Dermatology. 8th edn. Vol 2. Oxford: Wiley- Blackwell; 2010. p. 41.1-28.

Martins LCG, Horne M, Moreira DN, Follador I, Almeida VRP. Keratosis lichenoides chronica- case report. An Bras Dermatol. 2011;86:S148-51.

Adiflen E, Erdem O, Celipci S, Gurer MA. Easy to diagnose, difficult to treat: keratosis lichenoides chronica. Clin Exp Dermatol. 2008;35:47-50.

Masouye I, Saurat JH. Keratosis lichenoides chronica: the centenary of another Kaposi’s disease. Dermatology.1995;191:188-92.

Wozniacka A, Schwartz RA, Omulecki A, Lesiak A, Sysa- Jedrzejowska A. Keratosis lichenoides chronica: a diagnostic and therapeutic challenge. Clin Exp Dermatol.2006;31:48-50.

Margolis MH, Cooper GA, Johnson SA. Keratosis lichenoides chronica. Arch Dermatol.1984;120:1471-4.

Ruiz-MaldonadoR, Duran-McKinster C, Orozco-Covarrubias L, Saez-De-Oscariz M, Palacios-Lopez C. Keratosis lichenoides chronica in pediatric patients: a different disease?J Am Acad Dermatol.2007;56:S1-5.

Nijsten T, Mentens G, Lambert J. Vascular variant of Keratosis lichenoides chronica associated with hypothyroidism and response to tacalcitol and acitretin. Acta Derm Venereol.2002;82:128-30.

Demirci E, Boyvat A, Arica IE, Kocyigit P, Ozdemir E, Heper AO. Keratosis lichenoides chronica: marked response to PUVA in combination with acitretin. Acta Derm Venereol. 2005;85:552-3.

Muñoz-Santos C, Yébenes M, Romaní J, Luelmo J. Response of keratosis lichenoides chronica to efalizumab therapy.Arch Dermatol.2009;145:867-9.

Downloads

Published

2016-11-17

How to Cite

1.
Gupta SK, Monika D, Deepika D. Keratosis lichenoides chronica: case report. J Pak Assoc Dermatol [Internet]. 2016Nov.17 [cited 2025Jan.14];26(2):163-5. Available from: http://www.jpad.com.pk/index.php/jpad/article/view/62

Issue

Section

Case Reports

Most read articles by the same author(s)