Cutaneous variant of angiokeratoma corporis diffusum: a case report

Authors

  • Panchami Debbarman
  • Ashim Kumar Mondal
  • Niharika Ranjan Lal
  • Piyush Kumar
  • Ramesh Chandra Gharami

Keywords:

Angiokeratoma, angiokeratoma corporis diffusum

Abstract

Angiokeratoma corporis diffusum (ACD) is a rare clinical type of angiokeratoma and has been reported, mostly, in association with various life threatening conditions, of which Fabry disease is the most known. Rarely, it has been reported as an isolated finding without any systemic features. A 23-year-old male presented with numerous red papules of various sizes with a history of intermittent bleeding. Histopathology findings were consistent with angiokeratoma and our case was diagnosed as ACD. We herein present a case of cutaneous variant of ACD without any associated systemic associations. Also, the conditions associated with ACD have been briefly discussed. 

References

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Published

2016-12-15

How to Cite

1.
Debbarman P, Mondal AK, Lal NR, Kumar P, Gharami RC. Cutaneous variant of angiokeratoma corporis diffusum: a case report. J Pak Assoc Dermatol [Internet]. 2016Dec.15 [cited 2025Feb.7];23(3):331-4. Available from: http://www.jpad.com.pk/index.php/jpad/article/view/335

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Case Reports

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