Multiple familial trichoepitheliomas: A rare autosomal dominant skin tumor

Authors

  • Saba Latif PNS Shifa Hopital,Karachi

Keywords:

Familial, Trichoepithelioma, Basal cell carcinoma, Benign facial tumors, Appendageal tumors, Autosomal Dominant

Abstract

Multiple familial trichoepithelioma (MFT) is a rare autosomal dominant skin disease that presents as multiple small tumors, predominantly on face. The lesions resemble other types of skin diseases that present with papules and nodules. We present a patient with persistent eruptions of asymptomatic but cosmetically disfiguring papulonodular lesions on her face which histologically proved as lesions of trichoepitheioma. There was history of similar lesions in other family members too. She was managed with serial electrocautery, chemical cautery and medium depth chemical peel sessions.

References

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Published

2022-04-10

How to Cite

1.
Latif S. Multiple familial trichoepitheliomas: A rare autosomal dominant skin tumor. J Pak Assoc Dermatol [Internet]. 2022Apr.10 [cited 2024Jun.17];31(3):546-9. Available from: http://www.jpad.com.pk/index.php/jpad/article/view/1646

Issue

Section

Case Reports