Addison´s disease in a young child: A rare entity in children
Keywords:
Addison´s diseaseAbstract
Addison's disease is an adrenocortical insufficiency due to the dysfunction or destruction of the entire adrenal gland. The disease usually manifests when 90% or more of both adrenal cortices are dysfunctional or destroyed affecting both glucocorticoid and mineralocorticoid functions. The morbidity and mortality associated with Addisons disease is relatively high due to delay in diagnosis and initiation of therapy. Here, we report a case of a seven years old child who presented to us with diffuse hyperpigmentation of the body, body flexures, palmar creases and mucosae. He was diagnosed with Addison´s disease, which is indeed a rare entity. In addition, this case report will also enhance the importance of cutaneous examination in suspecting Addison´s disease.ÂReferences
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