A case of xanthoma disseminatum: A rare type of non–Langerhans cell histiocytosis


  • ATM Asaduzzaman
  • Md. Mostaque Mahmud
  • Muhammad Raquib Rahman
  • MA Wahab
  • Nadia Sharleen


Non-Langerhans cell histiocytosis, xanthoma disseminatum


Xanthoma disseminatum (XD) is a rare non-Langerhans cell histiocytosis that may involve skin, mucous membrane and internal organs. It manifests as symmetrically distributed, yellow-brown papules and nodules, involving face and flexures of body. We describe a case of XD in a 22-year-old female. She presented with multiple yellow-brown papules and plaques over face and body folds. Skin lesions were accompanied by visual disturbances. Examination revealed xanthomatous infiltration of cornea and oral mucosa. The case was confirmed with histopathological assessment. 


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How to Cite

Asaduzzaman A, Mahmud MM, Rahman MR, Wahab M, Sharleen N. A case of xanthoma disseminatum: A rare type of non–Langerhans cell histiocytosis. J Pak Assoc Dermatol [Internet]. 2018Dec.13 [cited 2024Jul.13];28(3):371-4. Available from: http://www.jpad.com.pk/index.php/jpad/article/view/1271



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